ICD-10 Coding for Down Syndrome(Q21.2U, Q90.0, Q90.0B)

Comprehensive guide to ICD-10 coding for Down syndrome, including nonmosaic, mosaic, and translocation types, with documentation requirements.

Also known as:
Trisomy 21Mongolism
Related ICD-10 Code Ranges

Complete code families applicable to Down Syndrome

Code Comparison: When to Use Each Code

Compare key differences between these codes to ensure accurate selection

CodeDescription
Q90.0Trisomy 21, nonmosaicism
Q90.1Trisomy 21, mosaicism
Q90.2Trisomy 21, translocation
Q90.9Down syndrome, unspecified

Clinical Decision Support

Always review the patient's clinical documentation thoroughly. When in doubt, choose the more specific code and ensure documentation supports it.

Key Information

Essential facts and insights aboutDown Syndrome

Differential Codes

Alternative codes to consider when ruling out similar conditions

Trisomy 21, mosaicismQ90.1
Trisomy 21, nonmosaicismQ90.0

Documentation & Coding Risks

Avoid these common issues when documenting Down Syndrome.

Failure to update code after genetic testing results.

Impact

Clinical: May lead to inappropriate treatment plans., Regulatory: Non-compliance with coding standards., Financial: Potential loss of reimbursement due to incorrect DRG.

Mitigation

Regularly review genetic testing results., Update codes promptly upon confirmation.

Using Q90.9 indefinitely without genetic confirmation.

Impact

Reimbursement: May lead to incorrect DRG assignment and reimbursement issues., Compliance: Non-compliance with coding guidelines., Data Quality: Impacts accuracy of patient records and data reporting.

Mitigation

Update to specific code (Q90.0, Q90.1, or Q90.2) once genetic testing confirms the type.

Genetic Testing Documentation

Impact

Lack of genetic testing documentation can lead to audit failures.

Mitigation

Ensure all genetic testing results are included in the patient's medical record.

Frequently Asked Questions